Types of EA

There are 5 types of EA. There are actually 2 different classification systems for these, the Gross and the Vogt, which are used interchangeably, by different medical centers. In medical terminology, “proximal” refers to a body part near the head (or towards the middle of the body, in the case of a limb), and “distal” refers to a body part farther from the head (or more towards the periphery of the body, in the case of a limb). The types are

	Isolated EA (Gross type A, Vogt type 2) Pure Esophageal Atresia, with no TEF. About 8% of EA patients have this type (which is also known as Gross type A, or Vogt type 2).
	EA with Proximal TEF (Gross type B, Vogt type 3A) EA, with a proximal TEF, or a TEF connecting between the upper pouch of the esophagus and the trachea. This is rare, with only about 0.8% of EA patients have this type. With this type of EA, food and saliva can travel directly into the lungs, before surgical correction is performed
	EA with Distal TEF (Gross type C, Vogt type 3B). EA, with a distal TEF, or a TEF connecting between the lower pouch of the esophagus and the trachea. This is by far the commonest type of EA, with about 89% of EA patients having this type. With this type of EA, gastric contents and acid can travel directly into the lungs, before surgical correction is performed.
	EA with Dual TEF’s (Gross type D, Vogt type 3C) Dual TEF, where there is both a TEF connecting between the upper pouch of the esophagus and the trachea, and a TEF connecting the lower pouch of the esophagus and the trachea. This is rare, with only about 1.4% of EA patients have this type.
	H-type TEF (no EA) (Gross type E) H-Type TEF, where there is a TEF connecting between the esophagus and the trachea, but there is no EA. Children with an H-Type TEF, unlike the other types, are often diagnosed later in infancy or childhood (and rarely as adults), rather than becoming evident shortly after birth. People with an H-type TEF can swallow, but often cough and choke during swallowing, especially with liquids, and may present with recurrent pneumonias. The exact prevalence of this form is not known (because they tend to be diagnosed late), but is thought to be about 4% (this is known as Gross type E).

 Tom Kovesi MD, Pediatric Respirologist, Children’s Hospital of Eastern Ontario, Ottawa, Ontario Canada
06/10/2013

Bibliography:

• Ebook Frontiers Update on EA-TEF Octobre 2017
  Usha Krishnan 1,2* and Christophe Faure 3,4
  1 Department of Pediatric Gastroenterology, Sydney Children’s Hospital, Sydney, NSW, Australia,
  2 Discipline of Pediatrics, School of Women’s and Children’s Health, University of New South Wales, Sydney, NSW, Australia,
  3 Division of Pediatric Gastroenterology, Sainte-Justine Hospital, Montreal, QC, Canada,
  4 Department of Pediatrics, Université de Montréal, Montreal, QC, Canada
  
  
• Long-term respiratory complications of congenital esophageal atresia with or without tracheoesophageal fistula: an update. May 2013
  Dis Esophagus. 2013 May-Jun;26(4):413-6.
  Kovesi T 5
  5 Department of Pediatrics, Children’s Hospital of Eastern Ontario, University of Ottawa, 401 Smyth Rd, Ottawa, ON, Canada. kovesi@cheo.on.ca

Esophageal Atresia Global Support Groups e.V. Sommerrainstrasse 61, 70374 Stuttgart, Germany